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重组小鼠过氧化物酶酰基辅酶A氧化酶1蛋白
产品名称:
重组小鼠过氧化物酶酰基辅酶A氧化酶1蛋白
英文名称:
Recombinant mouse ACOX1 protein, C-His
产品类别:
蛋白多肽
产品编号:
bs-42132P
保存条件:
Stored at -70℃ or -20℃. Avoid repeated freeze/thaw
[价格]
规格 价格 库存
100ug ¥ 2980.00 10
500ug ¥ 9500.00 10

产品详情

产品编号bs-42132P
英文名称Recombinant mouse ACOX1 protein, C-His
中文名称重组小鼠过氧化物酶酰基辅酶A氧化酶1蛋白
别????名ACOX1; ACOX1_HUMAN; ACOX1_MOUSE; AOX antibody Palmitoyl CoA oxidase; Palmitoyl-CoA oxidase; Peroxisomal acyl coenzyme A oxidase 1; Peroxisomal acyl-coenzyme A oxidase 1; SCOX; Straight chain acyl CoA oxidase; Straight-chain acyl-CoA oxidase.??
理论分子量31.8kDa
性????状Lyophilized or Liquid
浓????度>0.5mg/ml
物????种Mouse
序????列386-661/661
纯????度>90% as determined by SDS-PAGE
表达系统E.coli
活性Not tested
标签C-His
缓?冲?液20mM Tris-Hcl (pH=8.0)with 8M Urea
保存条件Stored at -70℃ or -20℃. Avoid repeated freeze/thaw cycles.
注意事项This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
产品介绍Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.

SWISS:
Q9R0H0

Gene ID:
11430

产品图片
The purity of the protein is greater than 90% as determined by reducing SDS-PAGE.

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